Abstract

Context Solid pseudopapillary neoplasms of the pancreas are extremely rare, accounting for 1-2% of primary pancreatic exocrine tumors and typically occur in women around the second or third decade of life. Tumors occurring in males are exceptionally uncommon. Case report We report herein a case of solid pseudopapillary neoplasm occurring in the pancreatic head in a forty-seven-year-old Hispanic male causing obstructive jaundice. The patient underwent endoscopic ultrasound and fine needle aspiration of the mass followed by endoscopic retrograde cholangiopancreatography with placement of biliary stents. He ultimately had a pancreatoduodenectomy with pathology confirming solid pseudopapillary neoplasm. Conclusion We discuss incidence, clinical presentation and overall survival of this rare lesion in male patients along with implications for post-operative surveillance.