Abstract

Context Pancreatic desmoplastic small round cell tumour (DSRCT) is an extremely rare malignancy of which very few reports exist. It follows an aggressive course and has a dismal prognosis. Case Report A twenty four - year - old male presented with a one month history of rapidly progressive obstructive jaundice associated with abdominal pain suggestive of a biliary colic. Method Contrast-enhanced CT (CECT) of the abdomen revealed a pancreatic head mass. He underwent a pancreatico-duodenectomy and adjuvant chemotherapy and is disease free one year after surgery. Conclusion This is the first reported case of a pancreatic head DSRCT, discovered in a young male investigated for a short history of painful obstructive jaundice.