Abstract

Context Polycystic disease is a rare disorder, which most commonly manifests in the kidney and liver. Recently an increased risk for pancreatic malignancies in subsets of patients with polycystic disease has been reported. Case report We report a patient with polycystic liver and kidney disease who successfully underwent a Whipple’s procedure for pancreatic adenocarcinoma. Conclusion Although technical difficulty may increase, pancreaticoduodenectomy can be safely performed in patients with polycystic liver disease.